Unicuspid Aortic Valve: An Adult Case Report
Published: 2022-01-11
Page: 30-34
Issue: 2022 - Volume 5 [Issue 1]
Amine Kherraf *
Department of Cardiology, University Hospital of Ibn Rochd, Casablanca, Morocco 1, Rue des Hôpitaux, Casablanca, Morocco.
Maha Bouziane
Department of Cardiology, University Hospital of Ibn Rochd, Casablanca, Morocco 1, Rue des Hôpitaux, Casablanca, Morocco.
Safia Ouarrak
Department of Cardiology, University Hospital of Ibn Rochd, Casablanca, Morocco 1, Rue des Hôpitaux, Casablanca, Morocco.
Ghali Bennouna
Department of Cardiology, University Hospital of Ibn Rochd, Casablanca, Morocco 1, Rue des Hôpitaux, Casablanca, Morocco.
Leila Azzouzi
Department of Cardiology, University Hospital of Ibn Rochd, Casablanca, Morocco 1, Rue des Hôpitaux, Casablanca, Morocco.
Rachida Habbal
Department of Cardiology, University Hospital of Ibn Rochd, Casablanca, Morocco 1, Rue des Hôpitaux, Casablanca, Morocco.
*Author to whom correspondence should be addressed.
Abstract
The unicuspid aortic valve is a very rare congenital disease that usually presents in the 3rd to 5th decade of life-and usually with severe aortic stenosis or regurgitation. Diagnosis can be made with 2- or 3-dimensional transthoracic or transesophageal echocardiography. It is mostly complicated by aortic dilatation and left ventricular hypertrophy. We present the case of a 35 years old, symptomatic patient with a unicuspid aortic valve, complicated by dilatation of the ascending aorta, with left ventricular hypertrophy.
Keywords: Aortic unicuspid valve, transesophaseal echocardiography, aortic dilation.