Pacemaker Implantation in a Rare Case of Situs Inversus Dextrocardia Using PRSVC Approach and Its Challenges
ALZEER ISLAM *
Mohammed V University, Rabat, Morocco and Cardiology B Department, Ibn Sina University Hospital Center, Morocco.
HILAL SAFAE
Mohammed V University, Rabat, Morocco and Cardiology B Department, Ibn Sina University Hospital Center, Morocco.
FELLAT IBTISSAM
Mohammed V University, Rabat, Morocco and Cardiology B Department, Ibn Sina University Hospital Center, Morocco.
CHERTI MOHAMED
Mohammed V University, Rabat, Morocco and Cardiology B Department, Ibn Sina University Hospital Center, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Situs inversus dextrocardia is a rare congenital anomaly that can complicate medical procedures, including the implantation of a dual-chamber pacemaker (PM). This case report describes the challenges encountered during pacemaker implantation in a patient with situs inversus dextrocardia and a complex venous anatomy, including a persistent right superior vena cava (RSVC) draining directly into the coronary sinus (CS) and a left-sided venous drainage with multiple turbulences. Despite the anatomical challenges, the procedure was successful, with pacemaker leads successfully placed in the left-sided right ventricle. This case highlights the importance of thorough preoperative assessment and understanding of venous variations in patients with situs inversus dextrocardia.
Keywords: Situs inversus dextrocardia, Persistent right superior vena cava, Atrioventricular block, Pacemaker implantation, Heterotaxy syndrome, Polysplenia