Lutembacher’s Syndrome: A Case Report from Hospital IBN Rochd of Casablanca, Morocco
Published: 2022-10-06
Page: 285-289
Issue: 2022 - Volume 5 [Issue 1]
B. E. Ovaga *
Department of Cardiology, University Hospital Center IBN Rochd, Casablanca, Morocco.
B. Mohammed Sidi
Department of Cardiology, University Hospital Center IBN Rochd, Casablanca, Morocco.
P. M. Mulendele
Department of Cardiology, University Hospital Center IBN Rochd, Casablanca, Morocco.
A. Fadoul
Department of Cardiology, University Hospital Center IBN Rochd, Casablanca, Morocco.
M. Njie
Department of Cardiology, University Hospital Center IBN Rochd, Casablanca, Morocco.
SI. Harouna
Department of Cardiology, University Hospital Center IBN Rochd, Casablanca, Morocco.
M. Haboub
Department of Cardiology, University Hospital Center IBN Rochd, Casablanca, Morocco.
L. Azzouzi
Department of Cardiology, University Hospital Center IBN Rochd, Casablanca, Morocco.
R. Habbal
Department of Cardiology, University Hospital Center IBN Rochd, Casablanca, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Lutembacher syndrome (LS) is a rare clinical entity, associated with acquired mitral stenosis (MS), congenital atrial septal defect (ASD). In the literature, other forms have been described including iatrogenic LS and reverse LS. LS is a condition with a female predominance, and, over-diagnosed, is badly suffering, making its particularity. The prognosis for this syndrome is best before the onset of pulmonary hypertension and right heart failure. LS is usually treated surgically by mitral valve surgery with concomitant closure of the atrial septal defect. We report in this case report, the observation of a 62-year-old woman consulting for dyspnea evolving for about a year, in a context of physical asthenia. Cardiac ultrasound led to the diagnosis of this rare clinical syndrome. The patient was referred for mitral valve replacement with ASD closure.
Keywords: Mitral stenosis (MS), Atrial Septal Defect (ASD), Lutembacher’s Syndrome (LS), Morocco
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References
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